Klippel-Trénaunay Weber Syndrome - “Clip Train Web”

• Neurocuteaneous disorder
• Ocular findings
• Congenital glaucoma (1)
•    Conjunctiva telangiectasias (2)
•    Vascular anomalies of the orbit, iris, retina, choroid and optic nerves
•    Gliomas of the optic nerve and chiasm
• Systemic findings
•   Limb hypertrophy (3) and increased length (4) with cutaneous nevus flammeus (Port Wine Stain) (5), hemangiomas and varicosities (6) of the affected limb
•    When associated with arteriovenous malformations (7) it is known as Klippel-Trénaunay Weber Syndrome